• Maha Al Dabbagh, Hanna Banjar, Nasser Galal, Amjad Kouatli, Hammam Kandil, and May Chehab.
• Department of Pediatric, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.
• Ann Thorac Med. 2014 Jul 1; 9 (Suppl 1): S113-20.

AbstractPulmonary hypertension (PH) is relatively uncommon in children. Pulmonary arterial hypertension (PAH) in pediatric comprises a wide spectrum of diseases, from a transient neonatal condition to a progressive disease associated with morbidity and mortality. Most common PAH in pediatric are idiopathic (IPAH) or PAH associated with congenital heart disease (PAH-CHD), while other associated conditions, such as connective tissue disease (CTD), are less common in pediatrics. Despite better understanding of PH and the availability of new medications during recent decades; the diagnosis, investigation and choice of therapy remain a challenge in children, as evidence-based recommendations depend mainly on adult studies. In this review, we provide a detailed discussion about the distinctive features of PAH in pediatric, mainly emphacysing on classification and diagnostic algorithm.

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