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Case Reports
Unilateral congenital facial nerve paralysis secondary to a benign epithelioid peripheral nerve sheath tumor.
- Michael P Ondik, Todd Preston, Javad Towfighi, and Jon E Isaacson.
- Division of Otolaryngology-Head and Neck Surgery, Penn State Milton S. Hershey Medical Center, Hershey, Pennsylvania, USA.
- Otol. Neurotol. 2007 Dec 1; 28 (8): 1091-3.
ObjectiveA benign epithelioid peripheral nerve sheath tumor is described in the setting of congenital facial nerve (FN) paralysis. This is the first reported case in the English literature.PatientA 10-month-old girl with unilateral congenital FN paralysis.InterventionsAuditory brainstem evoked potential study, gadolinium-enhanced magnetic resonance imaging, temporal bone computed tomography, and transmastoid FN decompression with tumor resection.Main Outcome MeasuresFollow-up for tumor recurrence and postoperative FN function.ResultsThe child underwent a transmastoid FN exploration with resection of a 0.6-cm spherical tumor analyzed to be a benign epithelioid peripheral nerve sheath tumor. There is no evidence of recurrence, and FN function was unchanged at 1 year postoperatively.ConclusionBenign epithelioid peripheral nerve sheath tumor can cause congenital facial nerve palsy.
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