• Leanne S Dahlgren, Sidney B Effer, Barbara C McGillivray, and Denise J Pugash.
• Department of Obstetrics and Gynaecology, University of British Columbia, Children's and Women's Hospital of British Columbia, Vancouver BC.
• J Obstet Gynaecol Can. 2006 Aug 1; 28 (8): 720-723.

BackgroundHereditary hemorrhagic telangiectasia (HHT) is a rare autosomal dominant condition. It is rarely seen in pregnancy and even more rarely has uterine manifestations.CaseA 29-year-old primigravid woman with HHT was noted to have vascular manifestations of her disease in the lower uterus, distal rectum, pelvis, and bladder before pregnancy. Prior to delivery, a case conference was held, involving representatives of the departments of vascular surgery, hematology, radiology, anaesthesiology, maternal-fetal medicine, neonatology, and laboratory medicine, and other appropriate health professionals. A successful elective Caesarean section was performed at term, with a good outcome for both mother and child.Conclusionregnancies in women with HHT and associated uterine vascular manifestations have been rarely reported, and published information is minimal. We present a case of a successful operative delivery following careful multidisciplinary antepartum care.

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