Laryngo- rhino- otologie
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Laryngo- rhino- otologie · Jun 2002
Case Reports[Infantile myofibromatosis of the tongue - a case-report].
We report a case of infantile myofibromatosis of the tongue in a 5 month old female child. The parents reported discovering the tumor in the musculature of the tongue and the tumor had largely grown in size in the space of 4 weeks. The child's health was not impaired at any time. After a specimen was removed for a histological examination, an infantile myofibromatosis was diagnosed. ⋯ The occurrence of these tumors in neonates and young children in the oral cavity and in particular in the tongue is rarely reported. Development of the benign tumor disease depends on the form of the tumor, which can be distinguished between a solitaire, a multiloculaire and a generalized form. In contrast to the other two forms, cases of generalized infantile myofibromatosis involve the visceral organs and have a poor prognosis with a mortality rate of 75 %. Spontaneous remission is often reported in the solitaire and multiloculaire varieties of infantile myofibromatosis.