Zhurnal voprosy neĭrokhirurgii imeni N. N. Burdenko
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Zh Vopr Neirokhir Im N N Burdenko · Apr 2010
Case Reports[Rare observation of hyperostotic cranial lesions in osteogenesis imperfecta].
A rare case of hyperostotic skull deformity in a patient with congenital bone defect--osteogenesis imperfecta--is described. In this case typical symptoms encountered in adults were observed: decreased body length caused by shortened extremities due to multiple pathological fractures in childhood, deformities of thorax, spine, facial bones and teeth, skull lesions with craniobasal and brainstem symptoms, bluish hue of sclera, hypoacusis etc.). In this patient non-typical abnormalities were found: visual deficit due to optic nerve atrophy caused by bilateral optic canal stenosis on the background of densitometrically proven hyperostotic skull base deformity.
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During recent decades many methods of spinal cord hypothermia (SCH) were developed. Nevertheless the problem of SCH in complex urgent care of patients with complicated spinal cord injuries remains unsolved as well as problems of tactics and techniques of hypothermia. ⋯ Own observations during the procedure were used as criteria for evaluation of effectiveness. Implementation of suggested technique is expected to increase quality of surgical treatment of patients with complicated spinal cord injury, to improve surgical outcomes and to decrease rate of disability.