American journal of respiratory and critical care medicine
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Am. J. Respir. Crit. Care Med. · Oct 2014
Pulmonary Hypertension in Cystic Fibrosis with Advanced Lung Disease.
The impact of pulmonary hypertension (PH) on survival in cystic fibrosis (CF) remains unclear. ⋯ The manifestation of PH is associated with significantly increased risk for death in CF patients with advanced lung disease.