• Abdelsimar T Omar, Jeric L Arbizo, Kimberly Mae C Ong, Christine Mae G Olivar, Jonathan P Rivera, Charlotte M Chiong, Arsenio Claro A Cabungcal, and KhuKathleen Joy OKJOSection of Neurosurgery, Department of Neurosciences, College of Medicine and Philippine General Hospital, Ermita, Manila, Philippines. Electronic address: kathleen.khu@neurosurgery.ph..
• Section of Neurosurgery, Department of Neurosciences, College of Medicine and Philippine General Hospital, Ermita, Manila, Philippines.
• World Neurosurg. 2020 Oct 1; 142: e260-e270.

ObjectiveChondroblastoma is an uncommon benign neoplasm of cartilaginous origin usually involving the long bones. The temporal bone is a rare location for this tumor. The clinical profile, optimal medical and surgical management, and outcomes of treatment for temporal bone chondroblastoma remain unknown.MethodsWe performed a systematic review of the SCOPUS, PubMed, and CENTRAL databases for case reports and case series on patients with histopathologically proven temporal bone chondroblastoma. Data on demographics, clinical manifestation, surgical management, adjuvant treatment, and outcome on last follow-up were collected.ResultsA total of 100 cases were reported in the literature, including one described in the current study. The mean age of patients was 42.3 years (range, 2-85 years), with a slight male predilection (1.3:1). The most common clinical manifestations were otologic symptoms (e.g., hearing loss [65%], tinnitus, and otalgia) and a palpable mass. Surgical excision was performed in all cases, with gross total excision achieved in 58%. Radiation therapy was performed in 18% of cases, mostly as adjuvant treatment after subtotal excision. There were no deaths at a median follow-up of 2 years. Among the patients with detailed status on follow-up, 58% had complete neurologic recovery, 38% had partial recovery, and 4% had progression of symptoms as a result of tumor recurrence.ConclusionsTemporal bone chondroblastoma has a distinct clinical profile from chondroblastoma of long bones. Surgery is the mainstay of treatment, and radiation therapy may be given after subtotal excision. Outcomes are generally favorable after treatment.Copyright © 2020 Elsevier Inc. All rights reserved.

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