-
Case Reports
Coexistence of Marfan-like Connective Tissue Disease with Morphologic Left Ventricular Non-Compaction.
- Satomi Yashima, Hiroyuki Takaoka, Togo Iwahana, Manami Takahashi, Yusuke Kondo, Hideki Ueda, Aya Saito, Yuya Ito, Noboru Motomura, Nobuyuki Hiruta, Jun-Ichiro Ikeda, Goro Matsumiya, and Yoshio Kobayashi.
- Department of Cardiovascular Medicine, Chiba University Graduate School of Medicine, Japan.
- Intern. Med. 2020 Dec 1; 59 (23): 3039-3044.
AbstractWe treated a man with co-incident Marfan-like connective tissue disease with morphologic left ventricular non-compaction (LVNC). He underwent valve-sparing aortic root replacement because of aortic root dilation at 43 years old. Pathological findings of the aorta revealed cystic medio-necrosis, consistent with Marfan syndrome. He developed congestive heart failure caused by LVNC at 47 years old. His daughter had scoliosis, and he had several physical characteristics suggestive of Marfan syndrome. We herein report a rare case of a patient who had Marfan-like connective disease with an LVNC appearance.
Notes
Knowledge, pearl, summary or comment to share?You can also include formatting, links, images and footnotes in your notes
- Simple formatting can be added to notes, such as
*italics*,_underline_or**bold**. - Superscript can be denoted by
<sup>text</sup>and subscript<sub>text</sub>. - Numbered or bulleted lists can be created using either numbered lines
1. 2. 3., hyphens-or asterisks*. - Links can be included with:
[my link to pubmed](http://pubmed.com) - Images can be included with:
 - For footnotes use
[^1](This is a footnote.)inline. - Or use an inline reference
[^1]to refer to a longer footnote elseweher in the document[^1]: This is a long footnote..