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Case Reports
Rare presentation of Rosai-Dorfman disease mimicking a cervical intramedullary spinal cord tumor.
- Mohamed El Molla, Tamadur Mahasneh, Sue-Ellen Holmes, and Darweesh Al-Khawaja.
- Neurosurgical Department, Wollongong Hospital, University of Wollongong, Wollongong, New South Wales, Australia.
- World Neurosurg. 2014 Feb 1;81(2):442.e7-9.
BackgroundRosai-Dorfman disease, or sinus histiocytosis with massive lymphadenopathy, is a rare, benign, lymphoproliferative disorder that commonly manifests as a massive painless cervical lymphadenopathy with associated fever and weight loss. Central nervous system involvement is extremely rare, and cervical spinal cord manifestation has not been reported.MethodsA 76-year-old man presented with a 10-week history of right hemiparesis. Magnetic resonance imaging identified an enhancing cervical intramedullary lesion consistent with a primary spinal cord tumor.ResultsHistopathology revealed intramedullary histiocytosis.ConclusionsThis cervical presentation of Rosai-Dorfman disease with central nervous system involvement suggests variation in the clinical manifestations of the disease, necessitating greater surgical awareness.Crown Copyright © 2014. Published by Elsevier Inc. All rights reserved.
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