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- Kristen A Warncke and Julie M Marshall.
- From the Department of Anesthesiology and Perioperative Medicine, University of Missouri, Columbia, Missouri.
- A A Pract. 2021 Jun 2; 15 (6): e01488.
AbstractKearns Sayre syndrome (KSS) is a rare mitochondrial myopathy that is associated with progressive impaired ventilatory drive, heart block, and peripheral neuropathy. Charcot-Marie-Tooth disease (CMT) is a rare chronic motor and sensory peripheral neuropathy which includes muscle weakness and restrictive pulmonary impairment. Patients with either condition having anesthesia can have postoperative respiratory failure. We report a 52-year-old man diagnosed with variants of KSS and CMT presenting for supraventricular tachycardia (SVT) ablation. This is the first report of successful perioperative management of a general anesthetic in a patient with both KSS and CMT.Copyright © 2021 International Anesthesia Research Society.
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