• Soumya Patra, Usha M K Rama Sastry, J Mahimaiha, Anand P Subramanian, Ravindranath K Shankarappa, and Manjunath C Nanjappa.
• 1Department of Cardiology,Sri Jayadeva Institute of Cardiovascular Sciences & Research,Bangalore,Karnataka,India.
• Cardiol Young. 2015 Jun 1; 25 (5): 861-7.

BackgroundCyanotic CHD comprises up to 25% of cases of all causes of CHD.RationaleThere is lack of data about the present spectrum of congenital cyanotic heart disease in the paediatric age group.ObjectiveThe present study was undertaken to determine the spectrum of patients with congenital cyanotic heart disease in the paediatric age group in tertiary paediatric cardiac care clinic.DesignProspective observational study.SettingPaediatric cardiac clinic of a tertiary cardiac care centre.MethodsAll children aged 0-18 years with suspected cyanotic CHD were provisionally included in this study. They underwent a thorough echocardiographic evaluation, and those patients who had definitive diagnosis of congenital cyanotic heart disease were included for final analysis.ResultsA total of 119 children met the inclusion criteria. Tetralogy of Fallot and its variant were the most common congenital cyanotic heart disease with proportion of about 44%. Other common malformations were double outlet right ventricle (14%), pulmonary atresia with ventricular septal defect (8%), total anomalous pulmonary venous connection (7%), d-transposition of the great arteries (9%), tricuspid valve anomalies--tricuspid atresia and Ebstein's anomaly--hypoplastic left-heart syndrome, truncus arteriosus, and complex CHD such as single ventricle.ConclusionTetralogy of Fallot and its variants were the most common cyanotic heart disease diagnosed in our patients. As there were a significant proportion of cases with complex cyanotic CHD, paediatric cardiologists should be familiar with the diagnosis and management of all these complex congenital malformations of the heart.

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