• Giselle Cuestas, Verónica Rodríguez, Flavia Doormann, Alejandra Pringe, Patricio Bellia Munzón, Gastón Bellia Munzón, Carlos Ortega, and Rubén Álvarez.
• Sección de Endoscopía Respiratoria, División de Otorrinolaringología, Hospital General de Niños "Dr. Pedro de Elizalde", Ciudad Autónoma de Buenos Aires, Argentina. giselle_cuestas@yahoo.com.ar.
• Arch Argent Pediatr. 2017 Apr 1; 115 (2): e120-e125.

AbstractWegener's granulomatosis is a necrotizing granulomatous vasculitis of autoimmune origin that primarily affects the upper and lower airways and kidneys. It is very rare in children and adolescents. When started at a young age it is often associated with subglottic stenosis. Subglottic stenosis is a potentially fatal manifestation of Wegener's granulomatosis. Its diagnosis requires a high index of suspicion since it might develop in the absence of other signs of activity. Occasionally, subglottic stenosis may present as the initial manifestation of the disease. Diagnosis is confirmed by endoscopic visualization of the lesion. The treatment is complex, and it often requires repeated interventions due to restenosis. We present a 13-year-old patient with subglottic stenosis secondary to Wegener's granulomatosis. We describe the clinical manifestations, diagnosis and treatment of this rare cause of respiratory distress in the pediatric population.Sociedad Argentina de Pediatría.

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