• Alexis Strickler, Silvanna Gallo, Pedro Jaramillo, and Gonzalo de Toro.
• Departamento de Pediatría, Universidad San Sebastián sede Puerto Montt, Puerto Montt, Chile. Electronic address: alexisstrickler@gmail.com.
• Rev Chil Pediatr. 2016 Jul 1; 87 (4): 279-83.

IntroductionMorphea or juvenile localised scleroderma (JLS) is an autoimmune, inflammatory, chronic, slowly progressive connective tissue disease of unknown cause that preferably affects skin and underlying tissues.ObjectiveTo report a case of Juvenil Localised scleroderma in an 8-year old girl, contributing to an early diagnosis and treatment.Clinical CaseThe case is presented of an 8 year-old girl who presented with indurated hypopigmented plaques, of linear distribution in the right upper extremity of two years onset, together with papery texture hyperpigmented indurated plaques with whitish areas of thinned skin in right lower extremity, and leg and ankle swelling. The clinical features and diagnostic tests, including histology were compatible with linear and pansclerotic JLS. She started with immunosuppressive therapy, physiotherapy, and occupational therapy.ConclusionsWe report a case of linear and pansclerotic ELJ type, in which there was a 2 year delay in diagnosis, however the response to treatment was positive as expected.Copyright © 2016 Sociedad Chilena de Pediatría. Publicado por Elsevier España, S.L.U. All rights reserved.

19 keywords...

hide…