• Sebastian Lippross, Konstantinos Tsaknakis, Heiko M Lorenz, and Anna K Hell.
• Klinik für Orthopädie und Unfallchirurgie, UKSH Campus Kiel, Kiel, Deutschland.
• Unfallchirurg. 2021 Sep 1; 124 (9): 755-767.

AbstractCongenital pseudarthrosis of the tibia (CPT) is a rare disease that has challenged trauma and orthopedic surgeons for a long time. Clinically CPT mostly presents with progressive varus and antecurvation malformation of the tibia in infancy and childhood. In many cases CPT is associated with neurofibromatosis or fibrous dysplasia. Without knowledge of the clinical picture a discontinuity of the tibia and/or fibula visible on an X‑ray can be misinterpreted as a simple fracture. Histopathological investigations have revealed that a pathological alteration of the periosteum in the region of the pseudarthrosis, a hamartoma, may be essentially responsible for this disorder. Consequently, to treat the CPT a resection of the hamartoma must also be carried out. Multimodal treatment approaches combining pharmacological and surgical treatment, such as the cross-union technique of Paley, seem to have improved the prognosis of CPT.© 2021. Springer Medizin Verlag GmbH, ein Teil von Springer Nature.

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