• Bo Xia, Chun Hong, Jing Tang, Cuifen Liu, and Gang Yu.
• Department of Maternal-Fetal Medicine, Guangdong Women and Children Hospital, Guangzhou, China.
• Medicine (Baltimore). 2017 Dec 1; 96 (51): e8915.

RationaleThe occurrence of congenital cystic adenomatoid malformation (CCAM) and vascular ring (VR) is extremely rare.Patient ConcernsWe present a case of left CCAM with VR consisting of a left aortic arch and right descending aorta with left tracheal compression causing atelectasis.DiagnosesA high-risk male neonate with the diagnosis of left CCAM was diagnosed at 20 weeks gestational age by antenatal ultrasound. Chest CT revealed multiple cysts in the left inferior lung. Cardiac CT showed VR consisting of a left aortic arch and right descending aorta with left tracheal compression causing atelectasis.Interventionsleft inferior lobectomy was performed. Cardiac CT showed VR consisting of a left aortic arch and right descending aorta with left tracheal compression causing atelectasis. Descending aorta transposition was performed.OutcomesThe patient recovered smoothly and remained asymptomatic during the 12-months of postoperative follow-up period.LessonsWe report this rare case of CCAM with VR consisting of left aortic arch and right descending aorta with left tracheal compression causing atelectasis. From the findings of this report, early surgical treatment is recommended. Although the prognosis after surgery remained good, second surgery can be avoided if VR was detected early.Copyright © 2017 The Authors. Published by Wolters Kluwer Health, Inc. All rights reserved.

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