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Case Reports
Anesthetic Management of Cardiopulmonary Bypass in Hutchinson-Gilford Progeria Syndrome: A Case Report.
- Katherine L Zaleski, Gregory S Matte, Monica E Kleinman, Ashwin Prakash, and Mary Lyn Stein.
- From the Departments of Anesthesiology, Critical Care and Pain Medicine.
- A A Pract. 2024 Aug 1; 18 (8): e01842e01842.
AbstractHutchinson-Gilford Progeria Syndrome (HGPS) is an ultrarare disorder of segmental premature aging that is associated with the development of advanced atherosclerosis and significant cardiovascular and cerebrovascular disease. Treatment with lonafarnib has improved survival in patients with HGPS; however, in extended longitudinal follow-up, there has been an increase in the prevalence of rapidly progressive calcific aortic stenosis. The evolving course of HGPS has prompted reconsideration of conservative management and led to the development of strategies for anatomic treatment. In this case report, we describe the anesthetic management of patients with HGPS undergoing surgical management of aortic stenosis with cardiopulmonary bypass.Copyright © 2024 International Anesthesia Research Society.
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