• Christian Espinoza S, Rafael Selman A, Felipe Pauchard T, Juan Rivera F, Sebastián Iturra U, Fernando Montecinos R, Héctor Eliash D, and Francisco Undurraga H.
• Servicio Cardiovascular, Instituto Nacional del Tórax, Hospital El Pino. cardiocirugia@clinicatabancura.cl
• Rev Med Chil. 2009 Jan 1; 137 (1): 9810098-100.

AbstractAortic dissection is a life-threatening disease that requires immediate surgical intervention. Marfan syndrome is a hereditary disease with an autosomal dominant transmission, which affects the connective tissue, with skeletal, cardiovascular and ocular involvement. It is one of the most prevalent connective tissue disorders, presenting a risk of aortic dissection of approximately 1% even without dilatation of the aorta. When dissection occurs during pregnancy and requires surgical intervention (type A dissection), maternal mortality is high (2096-30%). We report a 38 year-old woman with Marfan syndrome that had an acute type A aortic dissection and severe aortic regurgitation at 37 weeks of gestation. The patient underwent a cesarean section and delivered a healthy baby. Afterwards, aortic valve repair and ascending aortic replacement was successfully performed under circulatory arrest with deep hypothermia. Additionally mitral valve repair for degenerative disease with posterior, autologous pericardium mitral valve ring was performed.

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