• G Hsu, E Manabat, S Huffnagle, and H J Huffnagle.
• Department of Anesthesiology, Thomas Jefferson University Hospital, Philadelphia, PA 19107, USA. gch2p@hotmail.com
• Int J Obstet Anesth. 2011 Jan 1;20(1):82-5.

AbstractKlippel-Feil syndrome is believed to occur from failure of normal segmentation of cervical somites during gestation. We present the case of a 38-year-old primiparous woman with type III Klippel-Feil syndrome for elective cesarean delivery. Our patient had a short webbed neck, short stature, limited neck flexion and extension, and thoraco-lumbar abnormalities. A multidisciplinary approach, involving obstetrics, medical subspecialties, anesthesiology, otolaryngology, and radiology, were utilized to evaluate and manage this patient. Pulmonary function testing revealed a restrictive defect, but transthoracic echocardiography was normal without pulmonary hypertension. We planned a combined spinal-epidural technique; however, only the epidural technique was obtained. Cesarean delivery was commenced with favorable maternal and fetal outcomes. Post-operative pain management was provided with intravenous morphine patient-controlled analgesia.Copyright © 2010 Elsevier Ltd. All rights reserved.

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