• Nishant Dwivedi, Christie Michael, D Betty Lew, Sandra Arnold, Masanori Igarashi, Tulio Bertorini, Jerome W Thompson, Linda K Myers, and Monica L Brown.
• Departments of Microbiology, Immunology and Biochemistry, University of Tennessee Health Science Center, Memphis, TN 38163, United States.
• Int. J. Pediatr. Otorhinolaryngol. 2012 May 1;76(5):745-9.

AbstractJuvenile dermatomyositis (JDM) is the most common inflammatory autoimmune myopathy in children. Most common presentations consist of heliotrophic rash and/or gottron's papules in addition to proximal muscle weakness. A typical presentations have been reported. We present a 13-year-old African American male who presented with a two-week history of bilateral periorbital edema that was unresponsive to glucocorticoids. He had elevated transaminases but no detectable muscle weakness. A muscle biopsy was consistent with juvenile dermatomyositis. This case highlights the need to consider dermatomyositis in cases of facial swelling and the use of aggressive immunosuppressive therapies due to its associated vasculopathies.Published by Elsevier Ireland Ltd.

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