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Journal of anesthesia · Dec 2010
Case ReportsAnesthesia for a 16-month-old patient with Prader-Willi syndrome.
- Basak C Meco, Zekeriyya Alanoglu, Ozgur Sinan Cengiz, and Neslihan Alkis.
- Department of Anesthesiology and ICM, Faculty of Medicine, Ankara University, Mesa Koza sitesi, 2.blok no:15, GOP, 06700 Ankara, Turkey. basakceyda@hotmail.com
- J Anesth. 2010 Dec 1;24(6):949-50.
AbstractPrader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m² who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery.
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