• Braz J Anesthesiol · May 2014

    Case Reports

    Anesthesia for a patient with Fanconi anemia for developmental dislocation of the hip: a case report.

    • Zafer Dogan, Huseyin Yildiz, Ismail Coskuner, Murat Uzel, and Mesut Garipardic.
    • Department of Anesthesiology and Intensive Care, Bezmialem Vakif University Medical School, Istanbul, Turkey. Electronic address: drzdogan@yahoo.com.
    • Braz J Anesthesiol. 2014 May 1;64(3):201-4.

    AbstractFanconi anemia is a rare autosomal recessive inherited bone marrow failure syndrome with congenital and hematological abnormalities. Literature regarding the anesthetic management in these patients is limited. A management of a developmental dislocation of the hip was described in a patient with fanconi anemia. Because of the heterogeneous nature, a patient with fanconi anemia should be established thorough preoperative evaluation in order to diagnose on clinical features. In conclusion, we preferred caudal anesthesia in this patient with fanconi anemia without thrombocytopenia, because of avoiding from N2O, reducing amount of anesthetic, existing microcephaly, hypothyroidism and elevated liver enzymes, providing postoperative analgesia, and reducing amount of analgesic used postoperatively.Copyright © 2013 Sociedade Brasileira de Anestesiologia. Published by Elsevier Editora Ltda. All rights reserved.

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