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- P Hanusch, J Heyn, H Well, E Weninger, U Hasbargen, and M Rehm.
- Klinik für Anästhesiologie und Intensivmedizin, Klinikum der Universität München, Marchioninistr. 15, 81377, München.
- Anaesthesist. 2009 Jul 1; 58 (7): 691-4.
AbstractFriedreich's ataxia (FA) is a hereditary disease, which leads to degenerative changes in the spinal cord and cerebellum (incidence 1:50,000). These changes are caused by a defect in the gene that encodes a mitochondrial gene called frataxin and causes muscle weakness, scoliosis, cardiomyopathy and impaired glucose tolerance. Therefore, these patients require special care during anaesthesia. We report the case of a 25-year-old primigravida with a history of FA and dorsal stabilisation of the vertebral column, who was admitted to our hospital for elective caesarean section. Due to increased sensitivity to muscle relaxants, peridural anaesthesia with 8 ml 0.75% ropivacaine and 10 microg sufentanil was used in this case. The perioperative neurological consultation revealed no undue exacerbation of symptoms.
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