• Stefan J Grau, Markus Holtmannspoetter, Klaus Seelos, Joerg-Christian Tonn, and Axel Siefert.
• Department of Neursurgery, Klinikum Grosshadern, Ludwig-Maximilian-University Munich, Germany. Stefan.grau@med.uni-muenchen.de
• Spine. 2009 Jun 15; 34 (14): E498-500.

Study DesignCase report and clinical discussion.ObjectiveWe intend to report a very rare case of a giant spinal hemangioma causing myelopathy.Summary Of Background DataMultilevel symptomatic spinal hemangiomas causing acute neurologic symptoms are rare disorders. We found only sporadic reports in English literature.MethodsWe describe a very rare case in which Klippel-Trenaunay-Weber syndrome is associated with a multisegmental vertebral hemangioma causing a rapidly progressing thoracic myelopathy.ResultsBecause of the extension of the disease, surgical intervention was not feasible, the patient was treated by radiotherapy. The patient showed a complete regression of symptoms with stable condition after 3 months.ConclusionsIn extensive spinal hemangiomas, radiotherapy may represent a safe treatment modality with rapid clinical improvement even in cases with spinal cord compression. This report contributes to a wide range of known vascular abnormalities in Klippel-Trenaunay-Weber syndrome and supports the need for a careful multisystemic evaluation of these patients.

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