• Asifur Rahman, Haque Saif Ul SU Department of Neurosurgery, Bangabandhu Sheikh Mujib Medical University, Shahbag, Dhaka, Bangladesh., Bhandari Paawan Bahadur PB Department of Neurosurgery, Bangabandhu Sheikh Mujib Medical University, Shahbag, Dhaka, Bangladesh., and Shamsul Alam.
• Department of Neurosurgery, Bangabandhu Sheikh Mujib Medical University, Shahbag, Dhaka, Bangladesh. Electronic address: bijoun14@yahoo.com.
• World Neurosurg. 2017 Sep 1; 105: 1035.e5-1035.e10.

BackgroundCavum septum pellucidum (CSP), which is often found incidentally in a few populations, occasionally becomes symptomatic if enlarged significantly. Wilson disease (WD) is an uncommon autosomal recessive inborn defect in copper metabolism characterized by abnormal accumulation of copper in various tissues, particularly in the liver and the brain. Seizure disorder, although rare both in CSP and WD, may happen in a few patients with either of the conditions.Case DescriptionWe report a case of 17-year-old boy, a patient with known WD, who developed intractable seizure for a year, which was not controlled with a large amount of antiepileptics. Magnetic resonance imaging showed enlargement of his preexisting CSP, which was small and asymptomatic at the time of diagnosis of WD. His WD was in a state of remission when he developed the seizure disorder. On endoscopic cyst fenestration, he was relieved of the seizure.ConclusionsSymptomatic CSP is a rare disorder, but the coexistence of WD is even rarer. Endoscopic cyst fenestration is a novel procedure that can be successful in properly selected cases. To the best of our knowledge, CSP associated with WD has not been reported in any English literature. We present this case for its rarity along with a relevant literature review.Copyright © 2017 Elsevier Inc. All rights reserved.

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