Pulmonary hypertension and hepatic encephalopathy: lethal

J R Coll Physicians Edinb · Jan 2014

Case Reports

Pulmonary hypertension and hepatic encephalopathy: lethal complications of Rendu-Osler-Weber disease.

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by epistaxis, mucocutaneous telangiectasia with systemic manifestations due to visceral telangiectasia and arterio-venous malformations (AVMs). We describe unusual complications of HHT in a 68-year-old male who developed high-output cardiac failure with pulmonary hypertension in combination with hepatic encephalopathy due to hepatic AVMs. This case shows the importance of a multi-system approach to HHT and considers the treatment of its hepatic complications.

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- T J Ford, M W Fong, B C Cheah, and C Alexopolous.
- TJ Ford Prince of Wales Hospital Sydney NSW 2031 Australia. Email t.ford@unsw.edu.au.
- J R Coll Physicians Edinb. 2014 Jan 1; 44 (2): 126-9.
AbstractHereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by epistaxis, mucocutaneous telangiectasia with systemic manifestations due to visceral telangiectasia and arterio-venous malformations (AVMs). We describe unusual complications of HHT in a 68-year-old male who developed high-output cardiac failure with pulmonary hypertension in combination with hepatic encephalopathy due to hepatic AVMs. This case shows the importance of a multi-system approach to HHT and considers the treatment of its hepatic complications.

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Pulmonary hypertension and hepatic encephalopathy: lethal complications of Rendu-Osler-Weber disease.

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