• Jun Ma, Guijun Jia, Siyuan Chen, and Wang Jia.
• Department of Neurosurgery, Beijing Tiantan Hospital affiliated to Capital Medical University, Beijing, China; National Clinical Research Center for Neurological Diseases, Center of Brain Tumor, Beijing Institute for Brain Disorders and Beijing Key Laboratory of Brian Tumor, Beijing, China.
• World Neurosurg. 2019 Feb 1; 122: 16-23.

BackgroundDysplastic gangliocytoma of the cerebellum, also called Lhermitte-Duclos disease (LDD), is known as a rare, benign brain tumor. Around 200 cases have been reported.Case DescriptionHere we introduced a newly diagnosed adult case with intratumoral hemorrhage. Then we reviewed 18 cases diagnosed in our institute, including 12 adults and 6 children.ConclusionsPreoperative diagnosis based on magnetic resonance imaging is 50% in adults and 16.7% in pediatrics. Diagnostic tiger stripes are not always seen in pediatric cases. The prognosis of the disease is good if total resection can be achieved. Further examinations for PTEN mutation and other comorbidities are recommended.Copyright © 2018 Elsevier Inc. All rights reserved.

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