• Neth J Med · Apr 2020

    Case Reports

    Case series of three adult patients with exceptional clinical presentations of haemophagocytic lymphohistiocytosis.

    • M Khairoun, F Meynen, W Vercoutere, and H L Leavis.
    • Department of Rheumatology and Clinical immunology, University Medical Center Utrecht, Utrecht, the Netherlands.
    • Neth J Med. 2020 Apr 1; 78 (3): 136-141.

    AbstractMacrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still's disease.

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