Annales de cardiologie et d'angéiologie
-
Ann Cardiol Angeiol (Paris) · May 2020
Case Reports[A perimyocarditis revealing eosinophilic granulomatosis with polyangiitis].
Churg-Strauss syndrome (CSS) or eosinophilic granulomatosis with polyangiitis is a systemic vasculitis characterized by necrotizing arteritis, eosinophilic infiltration and extravascular granuloma; that may involve several organs. Cardiac involvement is the first cause of death in this vasculitis. These include myocarditis, pericarditis, coronary heart disease, dysrhythmias, and rarely valvular involvement. We report the observation of CSS revealed by acute perimyocarditis.