Klinische Monatsblätter für Augenheilkunde
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Klin Monbl Augenheilkd · Dec 2000
Case Reports[Langerhans-cell histiocytosis of the orbit; diagnosis, treatment and outcome in three patients -- children and adults].
Langerhans cell histiocytosis usually affects children. Systemic Langerhans cell histiocytosis may be present in 37% of affected children. Ten per cent of all children die of the disease. ⋯ Langerhans cell histiocytosis of the orbit is an important differential diagnosis of osteolytic and/or space-occupying lesions not only in children, but also in adults. A diagnostic biopsy followed by surgical excision and/or local and systemic corticoid- and chemotherapy are essential regarding the prognosis of local and systemic disease.