Respiratory investigation
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Respiratory investigation · Nov 2018
COPD assessment test as a possible tool for evaluating health-related quality of life in lymphangioleiomyomatosis.
Lymphangioleiomyomatosis (LAM) is a progressive, cystic lung disease that causes an obstructive ventilatory impairment similar to chronic obstructive pulmonary disease (COPD) and impairs the health-related quality of life (HRQoL). Here, we extended the use of the COPD assessment test (CAT) to patients with chronic respiratory diseases other than COPD. Specifically, the CAT was administered to patients with LAM for the first time. ⋯ Our results suggest that the CAT is a useful instrument for assessing HRQoL in sirolimus-treated patients with LAM.