Journal of the American Academy of Dermatology
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J. Am. Acad. Dermatol. · Jul 2016
Review Case ReportsSegmental stiff skin syndrome (SSS): A distinct clinical entity.
Stiff skin syndrome (SSS) is a noninflammatory, fibrosing condition of the skin, often affecting the limb girdles. ⋯ We propose a distinct clinical entity, segmental SSS, characterized by a segmental distribution, later age of onset, and less severe functional limitation. Both segmental SSS and widespread SSS share common diagnostic histopathologic features.
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J. Am. Acad. Dermatol. · Jul 2016
ReviewCutaneous manifestations of IgG4-related disease (RD): A systematic review.
IgG4-related disease (RD) is a recently described fibroinflammatory condition with both cutaneous and systemic manifestations. To our knowledge, the cutaneous manifestations have not been well characterized or systematically investigated to date in the literature. ⋯ Papules, plaques, and nodules of the head and neck appear to characterize patients with cutaneous IgG4-RD, which nevertheless usually presents with systemic manifestations.