International journal of pediatric otorhinolaryngology
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Int. J. Pediatr. Otorhinolaryngol. · Sep 2010
Case ReportsSevere form of hypoglossia-hypodactylia syndrome associated with complex cardiopathy: a case report.
Hypoglossia is a rare congenital anomaly and is frequently associated with limb anomalies. In 1971, Hall employed the term hypoglossia-hypodactylia syndrome for the classification of these oromandibular-limb hypogenesis syndromes. ⋯ We describe an unusual case of hypoglossia-hypodactylia syndrome. The newborn had hypoglossia, limb defects and complex congenital cardiopathy, which has to date never been reported to be associated to this syndrome.
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Int. J. Pediatr. Otorhinolaryngol. · Sep 2010
Case ReportsSpinal cord infarction following cricotracheal resection.
We report a case of an 18-year-old female who was referred to our institution after incurring a permanent quadriplegia resulting from spinal cord infarction following cricotracheal resection. Methods were case report and review of the literature. A tracheal stenosis had resulted from long-term intubation after premature birth, followed by tracheotomy after 1 year, surgical revision at 4 years of age and a spontaneous closure at the age of 6 after decannulation. ⋯ Immediate MRI should be performed if any abnormal findings are seen to verify the diagnosis. Quadriplegia in this setting likely resulted from compromised blood supply with concomitant edema, however, the exact cause of injury remains unclear: despite having chin-to-chest sutures, the patient's head remained in neutral position and was not in hyperflexion. Such an injury is likely more susceptible to steroid therapy if diagnosed as early as possible.
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Int. J. Pediatr. Otorhinolaryngol. · Sep 2010
A review of malpractice cases after tonsillectomy and adenoidectomy.
To examine sources of litigation following tonsillectomy and/or adenoidectomy. ⋯ A significant portion of malpractice claims following tonsillectomy or adenoidectomy are related to complications not commonly discussed in the literature.