Pediatric cardiology
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Pediatric cardiology · Jul 2007
Case ReportsLong-term support with milrinone prior to cardiac transplantation in a neonate with left ventricular noncompaction cardiomyopathy.
A 2-week-old female infant presented with acute decompensated left ventricular failure. Echocardiography diagnosed left ventricular noncompaction cardiomyopathy with dilated phenotype and a left ventricular shortening fraction <10%. ⋯ She was maintained on intravenous milrinone for 6 months until she underwent successful orthotopic heart transplantation. Young children can be supported with inotropes for prolonged periods while awaiting heart transplantation.
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Pediatric cardiology · Jul 2007
Case ReportsSingle coronary artery with fistula, right aortic arch, bicuspid aortic valve, and pulmonary stenosis: a rare combination.
We report a case of a 10-month-old Chinese girl with single left coronary artery, left coronary artery-to-right ventricle fistula, pulmonary stenosis, and right aorta arch with bicuspid aortic valve. The diagnosis was made by transthoracic echocardiography and confirmed by angiography. A surgical repair was performed with closure of the fistula at the point where it drained into the right ventricle plus a pulmonary valvulotomy.
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Diverticulum of Kommerell is an outpouching from the descending aorta that, along with an aberrant subclavian artery and ductus arteriosus, may form a vascular ring compressing the trachea and/or the esophagus. It has been reported as an incidental finding as well as the cause of persistent dysphagia, cough, "asthma," or airway compromise at various ages but has never been reported as a cause of esophageal atresia in a newborn. We present a newborn with diverticulum of Kommerell, a vascular ring, and esophageal atresia.