Archives des maladies du coeur et des vaisseaux
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Arch Mal Coeur Vaiss · Aug 1988
[Aortic media necrosis in Marfan's disease in young adults. Apropos of 5 surgically treated cases, with 3 survivals].
Five cases of Marfan's syndrome with cardiovascular lesions are presented. Among these five patients, two with type I aortic dissection, one with true aneurysm of the ascending aorta and one with aortic regurgitation underwent composite grafting of the ascending aorta according to the Bentall technique. The fifth patient died preoperatively, due to extensive dissection of the transverse aorta. ⋯ Fifty percent of the patients die at a mean age of 32 years, and 95 p. 100 of the deaths are caused by cardiovascular lesions. These lesions predominantly affect the left cardiac valves (aortic or mitral regurgitation) and the ascending aorta. Except in emergencies, replacement of the ascending aorta by a composite graft must be envisaged in subjects with Marfan's syndrome presenting with aortic regurgitation and dilatation of the aortic root.
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Arch Mal Coeur Vaiss · Aug 1988
Case Reports[The electrocardiogram and hypothermia. Apropos of a case].
Hypothermia induces characteristic electrocardiographic changes (Osborn wave). They have been observed in the animal and in man, both in accidental hypothermia and in hypothermia induced during cardiac surgery. ⋯ This case report is accompanied by a brief review of the literature. The recognition of these clinical signs should enable the diagnosis of hypothermia to be made at an early stage and appropriate treatment instituted, as this is a condition which is generally associated with a high mortality rate.