• E A Disu, O A Kehinde, A L Anga, P O Ubuane, A Itiola, I J Akinola, and B Falase.
• Department of Paediatrics, Lagos State University Teaching Hospital; Department of Paediatrics and Child Health, Lagos State University College of Medicine, Ikeja, Lagos, Nigeria.
• Niger J Clin Pract. 2019 Nov 1; 22 (11): 1621-1625.

AbstractCongenital pulmonary airway malformation (CPAM), formerly known as congenital cystic adenomatoid malformation (CCAM), is a rare developmental dysplastic lesion of the fetal tracheobronchial tree. CPAM is a rare cause of neonatal respiratory distress; however, its presence may span fetal to adult period. In two previous case-reports from Nigeria, CPAM was present in post-neonatal infants. We report the case of a neonate, who presented with increasing respiratory distress and an abnormal chest radiograph, initially assumed as pneumonic changes. A revised diagnosis of CPAM was made after a chest computed tomography (CT) scan. The neonate subsequently had a successful excision of the affected lobe with remarkable clinical improvement. The case highlights the need to utilize superior imaging studies such as CT when plain radiographs are inconclusive.

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