• Santosh Chaudhary, Vinayak Regmi, Sangeeta Shah, and Purbesh Adhikari.
• Department of Ophthalmology, B.P. Koirala Institute of Health Sciences, Dharan-18, Sunsari, Nepal.
• JNMA J Nepal Med Assoc. 2021 Jan 31; 59 (233): 77-80.

AbstractMedulloepithelioma is a rare childhood embryonal tumor arising from the non-pigmented ciliary epithelium of the pars plicata. We report a case of an 11-year-old male who presented with painless loss of vision of the right eye for the last three years and progressively increasing mass on the superior aspect of the globe for the last three months. On ocular examination, a firm, non-tender mass of 4cm x 3cm was noted in the superior aspect of the globe. CT-Scan of the orbit was suggestive of a foreign body with a haemorrhage or infection. The patient underwent enucleation with minimal manipulation. Histopathological examination of the enucleated globe revealed medulloepithelioma. The intraocular medulloepithelioma presentation is often late and masquerading, which may lead to extraocular extension and metastasis and ultimately unfavorable prognosis.

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