• Massimiliano Neroni, Roberto Gazzeri, Marcelo Galarza, and Alex Alfieri.
• Department of Neurosurgery, San Giovanni Addolorata Hospital, Rome, Italy.
• Spine. 2007 Oct 1; 32 (21): E608-10.

Study DesignCase report and clinical discussion.ObjectiveTo describe a rare case of intradural cervical disc herniation in a patient with Klippel-Feil syndrome (KFS).Summary Of Background DataKFS is a congenital spinal malformation characterized by the failure in segmentation of 2 or more cervical vertebrae. The development of a cervical disc herniation in a nonfused segment is uncommon. Intradural disc herniation is rare, with only 21 cases reported in the cervical region.MethodsWe present a case of a 52-year-old woman with KFS (C5-C6 fusion) who developed acute radiculopathy secondary to an intradural cervical disc herniation. Neurologic examination revealed a mild (Grade 3/5) decrease in motor function of the fingers and difficulty in performing fine motor tasks with right hand.ResultsThe patient underwent microsurgical removal of the herniated disc via an anterior approach followed by interbody fixation and anterior plating; exploration of the surgical field revealed 2 intradural disc fragments. After surgery, she experienced a complete remission of the symptoms.ConclusionTo our knowledge, this is the first case of intradural cervical disc herniation in a KFS patient described in the literature.

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