Marginal resection as a potential curative treatment option of

Medicine · Jul 2023

Case Reports

Marginal resection as a potential curative treatment option of infantile fibrosarcoma with good response after chemotherapy: A case report of an ETV6-NTRK3 positive infantile fibrosacroma of the distal tibia.

The infantile fibrosarcoma (IFS) is a non-rhabdomyosarcoma soft tissue sarcoma with locally aggressive properties. State of the art therapy consists of neoadjuvant chemotherapy followed by wide resection according to the criteria of the musculoskeletal tumor society. ⋯ An individual therapy for surgical treatment of IIFS is recommended. This comprises marginal resection in instead of the golden standard "wide resection" in selected cases.

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- Markus Weber, Frederik von Kunow, and Axel Hillmann.
- Faculty of Medicine, University of Regensburg, Regensburg, Germany.
- Medicine (Baltimore). 2023 Jul 7; 102 (27): e34194e34194.
RationaleThe infantile fibrosarcoma (IFS) is a non-rhabdomyosarcoma soft tissue sarcoma with locally aggressive properties. State of the art therapy consists of neoadjuvant chemotherapy followed by wide resection according to the criteria of the musculoskeletal tumor society.DiagnosesAn ETV6-NTRK3 positive IFS of the distal tibia in a 21-months old child showed good response to chemotherapy.InterventionsDue to refusal of amputation marginal resection completing the margins with a high speed drill and filling the space with bone cement was performed.OutcomesAt latest follow-up 10 years after surgery, no recurrence was observed.LessonsAn individual therapy for surgical treatment of IIFS is recommended. This comprises marginal resection in instead of the golden standard "wide resection" in selected cases.Copyright © 2023 the Author(s). Published by Wolters Kluwer Health, Inc.

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Marginal resection as a potential curative treatment option of infantile fibrosarcoma with good response after chemotherapy: A case report of an ETV6-NTRK3 positive infantile fibrosacroma of the distal tibia.

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