• Jose Basora, Jose Nieves, and Pedro Torrellas.
• Chest. 2014 Mar 1;145(3 Suppl):517A.

Session TitlePulmonary Hypertension Posters IISESSION TYPE: Poster PresentationsPRESENTED ON: Saturday, March 22, 2014 at 01:15 PM - 02:15 PMPURPOSE: In the last 30 years only a few countries have gone to pursue the development of a registry in Pulmonary Artery Hypertension in which the specific characteristics of their population is evaluated and classified. In Puerto Rico this kind of information has never been collected and analyzed. Data was obtained from the only available specialized clinic in pulmonary hypertension in the island to characterize the demographics and clinical course of the Puerto Rican population and to compare individuals according to classification subgroup, treatment strategies and outcome.MethodsProspective, multicenter, observational registry designed to characterize Puerto Rican's PAH adult patient subpopulation between July 1, 2012 and July 1, 2013.ResultsThis study is currently under final data collection with estimated completion date in November 2013. Partial results: A total of 57 patients (mean 61; range 20-84), 65% females and 35% males were entered in the registry. WHO Group 1 and 3 accounted for 70 and 19% of the population, respectively. Approximately 38% of our evaluated patients had an advanced clinical condition classified as WHO functional class III and IV. Regarding exercise tolerance of our subpopulation the mean six-minute walk test was 274m (range 129-441m).ConclusionsAs described in other studies we found a large number of our patients referred to our clinics in an advanced stage detected late in the course of the disease, with a majority of patients displaying severe functional and hemodynamic compromise.Clinical ImplicationsThe practical goal of the registry is to promote understanding about potential causes, recognize clinical and hemodynamic parameters, facilitate early and accurate diagnosis, and develop a more effective therapeutic approach.DisclosureThe following authors have nothing to disclose: Alvaro Aranda, Elba Martin, Ricardo Fernandez, Jose Nieves, Jose Basora, Pedro TorrellasNo Product/Research Disclosure Information.

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