Zhonghua Minguo xiao er ke yi xue hui za zhi [Journal]. Zhonghua Minguo xiao er ke yi xue hui
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Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi · Jul 1997
Case ReportsRetroperitoneal cystic lymphangioma: report of one case.
Cystic lymphangioma is a developmental malformation of the lymphatic system. It is extremely rare for this type of tumor to arise from retroperitoneum in newborns. ⋯ The clinical manifestation of chylous ascites may mimic retroperitoneal cystic lymphangioma. The finding in supine abdomen X ray and abdominal sonography may help us to make some differential diagnosis.
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Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi · Jul 1997
Multi-undulant T-U-wave, sinus bradycardia and long QT syndrome: a possible phenotype of mutant genes controlling the inward potassium rectifiers.
Inward rectifying potassium currents (Ikr and Iks) during phase 3 repolarization of the myocyte from the beginning to the end of repolarization of the myocardial syncytium will inscribe a T-U-wave on the surface electrocardiogram (ECG). Type two congenital long QT syndrome (LQT2) is a phenotype of human ether-a-go-go-related gene (HERG) mutation on the chromosome 7q 35-36. Type one congenital long QT syndrome (LQT1) is a phenotype of KvLQT1 mutation on the chromosome 11p15.5. ⋯ The RR intervals of these two probands of congenital LQT were somewhile more than 1200 ms during circadian waking time, while 31 cases without LQT showed their RR prolongation only during the circadian sleeping time. A multi-undulant T-U-wave, or a beat-to-beat changing of vectors or amplitudes of their T-U-wave observed in these two probands of congenital LQT, were not observable in those 31 patients without congenital LQT. Therefore, we concluded that multi-undulant T-U-wave, sinus bradycardia and a longer QTc was a phenotype of the mutated genes which control the inward rectifying potassium currents during phase 3 repolarization.