Anais brasileiros de dermatologia
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Rendu-Osler-Weber Syndrome also known as Hereditary Hemorrhagic Telangiectasia is a rare systemic fibrovascular dysplasia, with dominant autosomal inheritance. It is characterized by recurrent epistaxis, mucocutaneous telangiectasia, visceral arteriovenous malformation and positive family history. ⋯ Therapy is supportive and aimed at preventing complications. In this article we report a case of Rendu-Osler-Weber in a 64 year-old man, with history of mucocutaneous telangiectasia since the third decade of life, recurrent epistaxis, positive family history and vascular ectasia in the gastrointestinal tract.
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Comparative Study
Efficacy of gabapentin in the improvement of pruritus and quality of life of patients with notalgia paresthetica.
notalgia paresthetica is a subdiagnosed sensory neuropathy presenting as a condition of intense itching and hyperchromic macule on the back that interferes with daily habits. ⋯ Gabapentin is a good option for the treatment of severe itching caused by nostalgia paresthetica.
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Measuring the quality of life measure of patients with dermatologic diseases is an important concern. The instruments to evaluate it are commonly originally written in English and need to be translated and validated to be used in different cultures. ⋯ The Skindex-29 quality of life questionnaire was properly translated and validated to Brazilian Portuguese.